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George Budd and Hans Chiari reported the condition of inferior vena cava obstruction combined with hepatic vein or inferior vena cava thrombosis in 1845 and in 1899 respectively, we have defined this condition Budd-Chian syndrome, which is made up of ascites, hepatomegaly, and abdominal pain. This syndrome develops relatively acute symptoms and is combined with thrombosis of right hepatic vein. In 1950, Bennett reported inferior vena cava obstruction at the level of diaphragm as a similar condition, which clinically has a some different feature that develops symptoms lately, is found splenomegaly commonly, develops ascending collateral vessels, and is companied by membranous obstruction. He defined this idiopathic membranous obstruction of inferior vena cava (MOVC). Recently several cases were reported in Korea since 1978. Budd-Chian syndrome is rare but may be fatal because of liver cirrhosis and acute hepatic failure without treatment. We reported a case of MOVC treated by mesoatrial shunt with review of literature.
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